748 Congenital Anomalies of Respiratory System

Division of Community Health & Prevention
High Risk Infant Follow-Up
Program Manual For Local Health Departments
July 2010


Classification of Disease and Injuries

14. Congenital Anomalies (740-759)

748 Congenital Anomalies of Respiratory System

Excludes:

  • Congenital central alveolar hypoventilation syndome (327.25)
  • Congenital defect of diaphragm (756.6)
748.0 Choanal atresia
  • Atresia of nares (anterior)(posterior)
  • congenital stenosis of nares (anterior)(posterior)
748.1

Other anomalies of nose

  • Absent nose
  • Accessory nose
  • Cleft nose
  • Deformity of wall of nasal sinus 
  • Congenital:
    • deformity of nose
    • notching of tip of nose
    • performation of wall of nasal sinus

Excludes:

  • congenital deviation of nasal septum (754.0)
748.2 Web of larynx
  • Web of larynx
    • NOS
    • glottic
    • subglottic
748.3 Other anomalies of larynx, trachea, and bronchus
  • Absence or agenesis of:
    • bronchus
    • larynx
    • trachea
  • Anomaly (of):
    • cricoid cartilage
    • epiglottis
    • thyroid cartilage
    • tracheal cartilage
  • Atresia (of):
    • epiglottis
    • glottis
    • larynx
    • trachea
  • Cleft thyroid, cartilage, congenital
  • Congenital:
    • dilation, trachea
    • stenosis:
      • larynx
      • trachea
    • tracheocele
  • Diverticulum:
    • Bronchus
    • trachea
  • Fissure of epiglottis
  • Laryngocele
  • Posterior cleft of cricoid cartilage (congenital)
  • Rudimentary tracheal bronchus
  • Stridor, laryngeal, congenital
748.4

Congenital cystic lung

  • Disease, lung:
    • cystic, congenital
    • polycystic, congenital
  • Honeycomb lung, congenital

Excludes:

  • acquired or unspecified cystic lung (518.89)
748.5 Agenesis, hypoplasia, and dysplasia of lung
  • absence of lung (fissures)(lobe)
  • Aplasia of lung
  • Hypoplasia lung (lobe)
  • Sequestration of lung
748.6_

Other anomalies of lung

0  Anomaly of lung, unspecified

1  Congenital bronchiectasis

9  Other

  • Accessory lung (lobe)
  • Azygos lobe (fissure), lung
748.8 Other specified anomalies of respiratory system
  • Abnormal communication between pericardial and pleural sacs
  • Anomaly, pleural folds
  • Atresia of nasopharynx
  • Congenital cyst of mediastinum
748.9 Unspecified anomaly of respiratory system
  • Anomaly of respiratory system NOS